A rare case of heterotaxy and left ventricular non-compaction in an adult
نویسندگان
چکیده
Heterotaxy syndrome with left ventricular non-compaction is a rare co-existence of abnormalities with unknown cause. It can be isolated with no other associations, or associated with congenital heart diseases, or it can occur with multiple other congenital abnormalities. We describe the third reported case of heterotaxy syndrome with left ventricular non-compaction presenting in an adult.
منابع مشابه
سری موارد کاردیومیوپاتی Non compaction ایزوله بطن چپ
Isolated non compaction of left ventricular myocardium is a rare cardiomyopathy due to abnormalendomyocardialmorphogenesis. The incidence of non compaction cardiomyopathy in the general population has been estimated at 0.05% to 0.25% per year. NCCMP is a heart muscle disorder that is still little known among physicians and was first described in 1984 by engberding and bender. Echocardiograph...
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عنوان ژورنال:
دوره 27 شماره
صفحات -
تاریخ انتشار 2016